We report on a patient who presented to the ear, nose, and throat (ENT) clinic with swelling on the right side of the neck. Imaging studies revealed a large expansive heterogeneous process encroaching on the parapharyngeal region. Postintravenous contrast administration revealed an ovoid mass with moderate enhancement without affecting the parotid gland. The patient underwent full tumor resection, and a biopsy confirmed the presence of a malignant peripheral nerve sheath tumor (MPNST). In addition, as part of the treatment the patient received radiation therapy and is currently disease-free with no visible complications or signs of recurrence.