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Erschienen in: Wiener klinische Wochenschrift 19-20/2015

01.10.2015 | case report

Life-threatening acute pneumonitis in mixed connective tissue disease: a case report and literature review

verfasst von: Eva Rath, Shahin Zandieh, Alexander Löckinger, Mirko Hirschl, Klaus Klaushofer, Jochen Zwerina

Erschienen in: Wiener klinische Wochenschrift | Ausgabe 19-20/2015

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Summary

Mixed connective tissue disease (MCTD) is a rare connective tissue disease frequently involving the lungs. The main characteristic is a systemic sclerosis-like picture of slowly progressing interstitial lung disease consistent with lung fibrosis, while pulmonary arterial hypertension is rare. Herein, we present a case of a newly diagnosed MCTD patient developing life-threatening acute pneumonitis similar to lupus pneumonitis. Previous literature on this exceptionally rare complication of MCTD is reviewed and differential diagnosis and management discussed.
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Metadaten
Titel
Life-threatening acute pneumonitis in mixed connective tissue disease: a case report and literature review
verfasst von
Eva Rath
Shahin Zandieh
Alexander Löckinger
Mirko Hirschl
Klaus Klaushofer
Jochen Zwerina
Publikationsdatum
01.10.2015
Verlag
Springer Vienna
Erschienen in
Wiener klinische Wochenschrift / Ausgabe 19-20/2015
Print ISSN: 0043-5325
Elektronische ISSN: 1613-7671
DOI
https://doi.org/10.1007/s00508-015-0823-6

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