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Eur J Pediatr Surg 2024; 34(02): 137-142
DOI: 10.1055/a-2206-6837
Review Article

The French Experience with a Population-Based Esophageal Atresia Registry (RENATO)

Rony Sfeir 
1   Division of Gastroenterology, Hepatology and Nutrition, Department of Pediatrics, Reference Center for Congenital and Malformative Esophageal Disorders, Jeanne de Flandre Children's Hospital, Lille University Faculty of Medicine, Lille Cedex, Lille, France
,
Madeleine Aumar
1   Division of Gastroenterology, Hepatology and Nutrition, Department of Pediatrics, Reference Center for Congenital and Malformative Esophageal Disorders, Jeanne de Flandre Children's Hospital, Lille University Faculty of Medicine, Lille Cedex, Lille, France
,
Dyuti Sharma
1   Division of Gastroenterology, Hepatology and Nutrition, Department of Pediatrics, Reference Center for Congenital and Malformative Esophageal Disorders, Jeanne de Flandre Children's Hospital, Lille University Faculty of Medicine, Lille Cedex, Lille, France
,
Julien Labreuche
2   SEED: Statistique, Evaluation, Economique, Data-Management Maison Régionale de la Recherche Clinique University Hospital of Lille, France - Health Statistics, Lille, France
,
Luc Dauchet
3   Department of Epidemiology and Public Health, University Hospital of Lille, France - Public Health, Lille, France
,
Frederic Gottrand
1   Division of Gastroenterology, Hepatology and Nutrition, Department of Pediatrics, Reference Center for Congenital and Malformative Esophageal Disorders, Jeanne de Flandre Children's Hospital, Lille University Faculty of Medicine, Lille Cedex, Lille, France
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Abstract

This paper presented a national register for esophageal atresia (EA) started in January 2008. We report our experience about the conception of this database and its coordination. Data management and data quality are also detailed. In 2023, more than 2,500 patients with EA are included. Prevalence of EA in France was calculated at 1.8/10,000 live birth. Main clinical results are listed with scientific publications issued directly from the register.

Keywords

population-based register - esophageal atresia - rare disease


Publication History

Received: 05 November 2023

Accepted: 07 November 2023

Accepted Manuscript online:
08 November 2023

Article published online:
22 January 2024

© 2024. Thieme. All rights reserved.

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