Zusammenfassung
Die korrekte Interpretation von Hauterscheinungen kann die Diagnose zahlreicher seltener systemischer Erkrankungen erleichtern. Solchen Manifestationen können sowohl Autoimmunerkrankungen (Dermatomyositis, systemischer Lupus erythematodes, systemische Sklerodermie, Sarkoidose) als auch Stoffwechselerkrankungen (Porphyria cutanea tarda, Anderson-Fabry-Krankheit) zugrunde liegen. Andere Hauterscheinungen sind von großer Wichtigkeit, weil sie mögliche Warnzeichen okkulter Erkrankungen der inneren Organe sind. Dies gilt beispielsweise für einige Erkrankungen aus der Gruppe der neutrophilen Dermatosen (Pyoderma gangraenosum, Sweet-Syndrom).
Abstract
The correct interpretation of skin manifestations can facilitate the diagnosis of many rare systemic diseases. Such manifestations can be due to autoimmune diseases (e.g. dermatomyositis, systemic lupus erythematosus, systemic sclerosis and sarcoidosis) and metabolic diseases (e.g. Anderson-Fabry disease and porphyria cutanea tarda). Other cutaneous symptoms are of great importance because they are possible warning signs of occult diseases of internal organs. This is true for example for some diseases from the group of neutrophilic dermatoses, such as Sweet’s syndrome and pyoderma gangraenosum.
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Gualtieri, B., Hertl, M. Seltene Erkrankungen an der Haut erkennen. Internist 60, 193–201 (2019). https://doi.org/10.1007/s00108-018-0548-5
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DOI: https://doi.org/10.1007/s00108-018-0548-5
Schlüsselwörter
- Hautzeichen innerer Erkrankungen
- Autoimmunerkrankungen
- Stoffwechselerkrankungen
- Sweet-Syndrom
- Livedo reticularis