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Muskelerkrankungen und Erkrankungen peripherer Nerven im Erwachsenenalter

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Neuroorthopädie - Disability Management

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Zusammenfassung

Sowohl Myopathien als auch Neuropathien bzw. Neuronopathien gehen vielfach mit Paresen, Atrophien, Hypotonie und eingeschränkter Mobilität einher. Dies kann bereits intrauterin zu verminderten Kindsbewegungen und damit zu Kontrakturen führen. Postnatal führen klinische Manifestationen von Myopathien und Neuropathien zu neuroorthopädischen Krankheitsbildern wie Fehlstellungen, Kontrakturen, Luxationen, Subluxationen oder Arthrosen. Myopathien, die im Erwachsenenalter beginnen oder bis ins Erwachsenenalter dauern und mit orthopädischen Komplikationen einhergehen, sind die Gliedergürtel-Muskeldystrophien, die Emery-Dreifuss-Muskeldystrophie, die myotonen Dystrophien, die myofibrillären Myopathien, die metabolischen Myopathien und einige seltene Myopathien. Unter den Neuronopathien geht vor allem die ALS mit orthopädischen Problemen einher. Bei den meisten hereditären Neuropathien entwickeln sich Fußdeformitäten.

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Authors and Affiliations

  1. Krankenanstalt Rudolfstiftung. Messerli Institut, Wien, Österreich

    Josef Finsterer

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  1. Josef Finsterer
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Editors and Affiliations

  1. Institut MOTIO für Kinder- und Neuroorthopädie, Wien, Österreich

    Walter Michael Strobl

  2. Augsburg, Deutschland

    Nils Schikora

  3. Veitshöchheim, Deutschland

    Elisabeth Pitz

  4. Feucht, Deutschland

    Claudia Abel

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Finsterer, J. (2021). Muskelerkrankungen und Erkrankungen peripherer Nerven im Erwachsenenalter. In: Strobl, W.M., Schikora, N., Pitz, E., Abel, C. (eds) Neuroorthopädie - Disability Management. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-61330-6_12

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  • DOI: https://doi.org/10.1007/978-3-662-61330-6_12

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  • Print ISBN: 978-3-662-61329-0

  • Online ISBN: 978-3-662-61330-6

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