Abstract
All forms of epidermolysis bullosa (EB) are characterized by skin fragility and cutaneous injury. Hence, wound healing is the dominant issue of disease management in all types of EB. Due to ongoing blistering, persistent inflammatory activity, polymicrobial colonization with frequent infections, poor nutritional status, and oxygen supply, EB lesions often become chronic, non-healing wounds. This causes considerable pain, daily extended wound dressings with costs to the patient, family, and healthcare providers [36].
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Lanschuetzer, C.M. et al. (2009). Therapeutical Approaches. In: Fine, JD., Hintner, H. (eds) Life with Epidermolysis Bullosa (EB). Springer, Vienna. https://doi.org/10.1007/978-3-211-79271-1_3
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