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Erschienen in: European Surgery 6/2020

22.10.2020 | case report

Refractory hypoglycemia associated with giant solitary fibrous tumor of the pleura (Doege–Potter syndrome)

verfasst von: Carlo Alberto Manzo, Emanuele Asti, Caterina Froiio, Barbara Bruni, Luigi Bonavina, MD

Erschienen in: European Surgery | Ausgabe 6/2020

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Summary

Background

The association of a solitary tumor of the pleura with paraneoplastic refractory hypoglycemia is a very rare clinical condition.

Methods

An 86-year-old gentleman with an incidentally discovered large mass in the left chest and a long-standing history of refractory hypoglycemia was referred for surgical consultation. Computed tomography and PET (Positron Emission Tomography) scan confirmed the presence of a homogeneous mass leaning on the left hemidiaphragm with no tracer uptake.

Results

After tumor board discussion, the mass was radically excised through a left thoracotomy. Histopathology revealed a benign solitary fibrous tumor of the pleura. At 1‑year follow-up the patient was doing well and did not further complain of hypoglycemia-related symptoms.

Conclusion

Doege–Potter syndrome is a life-threatening condition associated with severely impaired quality of life. Prompt identification and surgical treatment are mandatory.
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Metadaten
Titel
Refractory hypoglycemia associated with giant solitary fibrous tumor of the pleura (Doege–Potter syndrome)
verfasst von
Carlo Alberto Manzo
Emanuele Asti
Caterina Froiio
Barbara Bruni
Luigi Bonavina, MD
Publikationsdatum
22.10.2020
Verlag
Springer Vienna
Erschienen in
European Surgery / Ausgabe 6/2020
Print ISSN: 1682-8631
Elektronische ISSN: 1682-4016
DOI
https://doi.org/10.1007/s10353-020-00673-w

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