Solid pseudopapillary tumours, also known as Frantz’s tumours, are rare pancreatic lesions which usually occur in young 20–30 year-old women. They account for about 2% of all exocrine pancreatic tumours. They often present with vague abdominal pain and the diagnosis is frequently an incidental finding.
In this case series and narrative review, we attempt to update the current standpoint on primary pseudopapillary tumours. In this paper we present a case series of three subjects (2 females and 1 male) who were diagnosed with primary pseudopapillary tumours. Their treatment and follow-up is described in detail.
These tumours will be discussed in the context of a literature review.
Surgical resection remains the primary method of treatment for this subtype of pancreatic tumours. The prognosis is excellent in patients who undergo resection.