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CC BY-NC-ND 4.0 · Indian J Med Paediatr Oncol 2009; 30(01): 39-42
DOI: 10.4103/0971-5851.56336
CASE REPORT

Melorheostosis with renal arterio-venous malformation: A case report with review of literature

Abdul Rashid Lone
Department of Medical Oncology, RCC, Sheri Kashmir Institute of Medical Sciences, Srinagar, Kashmir, India
,
Mushtaq Ahmad
Department of Medical Oncology, RCC, Sheri Kashmir Institute of Medical Sciences, Srinagar, Kashmir, India
,
Sheikh Aejaz Aziz
Department of Medical Oncology, RCC, Sheri Kashmir Institute of Medical Sciences, Srinagar, Kashmir, India
,
Gul Mohammad Bhat
Department of Medical Oncology, RCC, Sheri Kashmir Institute of Medical Sciences, Srinagar, Kashmir, India
,
Javid Rasool Bhat
Department of Clinical Hematology, RCC, Sheri Kashmir Institute of Medical Sciences, Srinagar, Kashmir, India
,
Rifat Jahan
Department of Medical Oncology, RCC, Sheri Kashmir Institute of Medical Sciences, Srinagar, Kashmir, India
,
Shoukat H Khan
Department of Nuclear Medicine, RCC, Sheri Kashmir Institute of Medical Sciences, Srinagar, Kashmir, India
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Abstract

Melorheostosis, also known as Leri′s disease and flowing periosteal hyperostosis, is a rare cause of pain and stiffness in a limb. The appearance is of "candle greasing" down one side of one or several bones of the body. We describe a case referred to tertiary care center with suspicion of renal cell carcinoma with diffuse bone metastasis. After reassessment, the patient was diagnosed melorheostosis with renal AV malformation. He was reassured about the benign nature of the disease and is asymptomatic.

Keywords

Flowing periosteal hyperostosis - Leri′s disease - melorheostosis - renal AV malformation


Publication History

Article published online:
19 November 2021

© 2009. Indian Society of Medical and Paediatric Oncology. This is an open access article published by Thieme under the terms of the Creative Commons Attribution-NonDerivative-NonCommercial-License, permitting copying and reproduction so long as the original work is given appropriate credit. Contents may not be used for commercial purposes, or adapted, remixed, transformed or built upon. (https://creativecommons.org/licenses/by-nc-nd/4.0/.)

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