Risk of Development of Abdominal Aortic Aneurysm and Dissection of Thoracic Aorta in a Postpartum Womanwith Marfans Syndrome

Aki Tomihara; Naoto Ashizawa; Kuniko Abe; Naoe Kinoshita; Keisuke Chihaya; Tsuyoshi Yonekura; Satoki Fukae; Kazuto Ashizawa; Kiyoyuki Eishi; Tomayoshi Hayashi; Katsusuke Yano

doi:10.2169/internalmedicine.45.1880

CASE REPORTS

Risk of Development of Abdominal Aortic Aneurysm and Dissection of Thoracic Aorta in a Postpartum Womanwith Marfans Syndrome

Aki Tomihara, Naoto Ashizawa, Kuniko Abe, Naoe Kinoshita, Keisuke Chihaya, Tsuyoshi Yonekura, Satoki Fukae, Kazuto Ashizawa, Kiyoyuki Eishi, Tomayoshi Hayashi, Katsusuke Yano

Author information

Aki Tomihara
Department of Pathology, Nagasaki University Hospital
Naoto Ashizawa
Division of Cardiovascular Medicine, Graduate School of Biomedical Sciences, Nagasaki University
Kuniko Abe
Department of Pathology, Nagasaki University Hospital
Naoe Kinoshita
Department of Pathology, Nagasaki University Hospital
Keisuke Chihaya
Department of Pathology, Nagasaki University Hospital
Tsuyoshi Yonekura
Division of Cardiovascular Medicine, Graduate School of Biomedical Sciences, Nagasaki University
Satoki Fukae
Division of Cardiovascular Medicine, Graduate School of Biomedical Sciences, Nagasaki University
Kazuto Ashizawa
Department of Radiology, Nagasaki University Hospital
Kiyoyuki Eishi
Division of Cardiovascular Surgery, Graduate School of Biomedical Sciences, Nagasaki University
Tomayoshi Hayashi
Department of Pathology, Nagasaki University Hospital
Katsusuke Yano
Division of Cardiovascular Medicine, Graduate School of Biomedical Sciences, Nagasaki University

Keywords: Marfans syndrome, postpartum, abdominal aortic aneurysm, descending thoracic aortic dissection

JOURNAL OPEN ACCESS

2006 Volume 45 Issue 22 Pages 1285-1289

DOI https://doi.org/10.2169/internalmedicine.45.1880

Details

Abstract

A 24-year-old pregnant woman with Marfans syndrome delivered by cesarean section during the 38th week of gestation. Although aortic root dilatation did not increase during pregnancy, three months after delivery, the patient noticed a pulsatile abdominal mass. Aortic aneurysm was diagnosed and surgical replacement of the infrarenal abdominal aorta to the common iliac arteries and reconstruction of the inferior mesenteric artery were performed. Moreover, the patient subsequently developed a Stanford type B thoracic aortic dissection, even after more than four months of β-blockade.

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