Chest
Selected ReportsA Case of Variant Scimitar Syndrome
Section snippets
Case Report
In February 2007, a 25-year-old man complained of dyspnea classified as New York Heart Association II. He was a current smoker (10 pack-years), reporting one episode of hemoptysis after physical effort and pneumonia 5 years ago. Standard radiography showed right hilar anomalies. Spirometry showed that FEV1 was 2.6 L (56% predicted) and FVC was 3.56 L (64% predicted). FEV1/FVC, forced expiratory flow at 75%, forced expiratory flow at 25% to 75%, and residual volume were 80%, 45%, 39%, and 124%
Discussion
The patient presented dyspnea related to restrictive syndrome, tobacco intake, and lack of physical activity. Hemoptysis was probably related to systemic vascularization, although in this case, systemic arterial supply was not nearby the bronchi.
Description and classification of these anatomic anomalies is difficult. This is a case of scimitar syndrome, as defined by hypogenetic lung with PAPVR. However, anomalous venous drainage is not into the IVC, as usually described in scimitar syndrome,
Acknowledgments
Financial/nonfinancial disclosures: The authors have reported to CHEST that no potential conflicts of interest exist with any companies/organizations whose products or services may be discussed in this article.
Other contributions: We thank Sylvain Ordureau, Useful Progress, and Paris-Descartes University for allowing us to use the Volviz software for three-dimensional reconstruction. We also thank Sophie Thébaud for correcting the English.
References (5)
- et al.
Meandering right pulmonary vein simulating the Scimitar syndrome
Chest
(1972) - et al.
Two cases of scimitar variant
Chest
(1994)
Cited by (0)
Reproduction of this article is prohibited without written permission from the American College of Chest Physicians. See online for more details.