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18.04.2023 | short communication

Hemispherotomy in an infant with hemimegalencephaly and Ohtahara syndrome

verfasst von: Katarina Pavičić Klancir, Prof. Dubravko Habek, MD, MSc, PhD, PhD, Vlasta Đuranović, Ana Tripalo Batoš, Sanja Pejić Roško, Milan Stanojević

Erschienen in: Wiener Medizinische Wochenschrift

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Summary

We represent the case of a premature twin neonate born from uncomplicated pregnancy who developed seizures at the age of 24 h. Two-dimensional ultrasound and magnetic resonance imaging revealed left-sided hemimegalencephaly. Further extensive diagnostic evaluation revealed a diagnosis of Ohtahara syndrome. Resistance of the seizures to antiepileptic therapy led to hemispherotomy that was performed at the age of 10 months. Our patient is now a 4-year-old child, walking, eating without a nasogastric tube, still with right hemiparesis and lateral strabismus but without seizures.
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Metadaten
Titel
Hemispherotomy in an infant with hemimegalencephaly and Ohtahara syndrome
verfasst von
Katarina Pavičić Klancir
Prof. Dubravko Habek, MD, MSc, PhD, PhD
Vlasta Đuranović
Ana Tripalo Batoš
Sanja Pejić Roško
Milan Stanojević
Publikationsdatum
18.04.2023
Verlag
Springer Vienna
Erschienen in
Wiener Medizinische Wochenschrift
Print ISSN: 0043-5341
Elektronische ISSN: 1563-258X
DOI
https://doi.org/10.1007/s10354-023-01009-5