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18.04.2023 | short communication

Hemispherotomy in an infant with hemimegalencephaly and Ohtahara syndrome

Erschienen in: Wiener Medizinische Wochenschrift

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Summary

We represent the case of a premature twin neonate born from uncomplicated pregnancy who developed seizures at the age of 24 h. Two-dimensional ultrasound and magnetic resonance imaging revealed left-sided hemimegalencephaly. Further extensive diagnostic evaluation revealed a diagnosis of Ohtahara syndrome. Resistance of the seizures to antiepileptic therapy led to hemispherotomy that was performed at the age of 10 months. Our patient is now a 4-year-old child, walking, eating without a nasogastric tube, still with right hemiparesis and lateral strabismus but without seizures.
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Metadaten
Titel
Hemispherotomy in an infant with hemimegalencephaly and Ohtahara syndrome
Publikationsdatum
18.04.2023
Erschienen in
Wiener Medizinische Wochenschrift
Print ISSN: 0043-5341
Elektronische ISSN: 1563-258X
DOI
https://doi.org/10.1007/s10354-023-01009-5