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18.04.2023 | short communication

Hemispherotomy in an infant with hemimegalencephaly and Ohtahara syndrome

verfasst von: Katarina Pavičić Klancir, Prof. Dubravko Habek, MD, MSc, PhD, PhD, Vlasta Đuranović, Ana Tripalo Batoš, Sanja Pejić Roško, Milan Stanojević

Erschienen in: Wiener Medizinische Wochenschrift | Ausgabe 5-6/2024

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Summary

We represent the case of a premature twin neonate born from uncomplicated pregnancy who developed seizures at the age of 24 h. Two-dimensional ultrasound and magnetic resonance imaging revealed left-sided hemimegalencephaly. Further extensive diagnostic evaluation revealed a diagnosis of Ohtahara syndrome. Resistance of the seizures to antiepileptic therapy led to hemispherotomy that was performed at the age of 10 months. Our patient is now a 4-year-old child, walking, eating without a nasogastric tube, still with right hemiparesis and lateral strabismus but without seizures.

Vorheriger Artikel Olfactory identification, cognition, depressive symptoms, and 5-year mortality in patients with subjective cognitive decline, mild cognitive impairment, and Alzheimer’s disease

Nächster Artikel Scale for the assessment and rating of ataxia (SARA): Übersetzung und kulturelle Anpassung an den deutschsprachigen Raum

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Titel: Hemispherotomy in an infant with hemimegalencephaly and Ohtahara syndrome
verfasst von: Katarina Pavičić Klancir
Prof. Dubravko Habek, MD, MSc, PhD, PhD
Vlasta Đuranović
Ana Tripalo Batoš
Sanja Pejić Roško
Milan Stanojević
Publikationsdatum: 18.04.2023
Verlag: Springer Vienna
Erschienen in: Wiener Medizinische Wochenschrift / Ausgabe 5-6/2024
Print ISSN: 0043-5341
Elektronische ISSN: 1563-258X
DOI: https://doi.org/10.1007/s10354-023-01009-5

Springer Medizin Österreich

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