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Erschienen in: Spektrum der Augenheilkunde 5/2014

01.11.2014 | case report

Histology after enucleation with Sturge–Weber syndrome

verfasst von: Dr. Fabian Mathias Bauer, Johann Colvin, Max Rasp, Eva Maria Krall, Eva Maria Arlt, Alexander Bachernegg, Alois Dexl, Martin Emesz

Erschienen in: Spektrum der Augenheilkunde | Ausgabe 5/2014

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Summary

At terminal stage, Sturge–Weber syndrome (SWS) can lead to choroidal calcification due to local chronic ischemia caused by congenital vascular malformation. We report a 51-year-old male with known SWS, who presented to the University of Salzburg eye clinic with chronic pain in the left eye. Upon examination, endophthalmitis, total retinal detachment, and complete loss of vision were diagnosed. Enucleation was performed due to the progression of the disease. During the procedure, ossification of the choroid was seen macroscopically. Histological examination revealed lamellar bone with yellow bone marrow.
Literatur
1.
Zurück zum Zitat Stranzinger E, Huisman TA. Sturge–Weber syndrome. Early manifestation and visualization of disease course. Radiologe. 2007;47(12):1126–30.PubMedCrossRef Stranzinger E, Huisman TA. Sturge–Weber syndrome. Early manifestation and visualization of disease course. Radiologe. 2007;47(12):1126–30.PubMedCrossRef
2.
Zurück zum Zitat Monselise M, Rapaport I, Romem M, Barishak YR. Intraocular ossification. Ophthalmologica. 1985;190:225–9.PubMedCrossRef Monselise M, Rapaport I, Romem M, Barishak YR. Intraocular ossification. Ophthalmologica. 1985;190:225–9.PubMedCrossRef
3.
Zurück zum Zitat Grisanti S, Guidry C. Transdifferentiation of retinal pigment epithelial cells from epithelial to mesenchymal phenotype. Invest Ophthalmol Vis Sci. 1995;36:391–405.PubMed Grisanti S, Guidry C. Transdifferentiation of retinal pigment epithelial cells from epithelial to mesenchymal phenotype. Invest Ophthalmol Vis Sci. 1995;36:391–405.PubMed
4.
Zurück zum Zitat Iwach AG, Hoskins HD, Jr., Hetherington J, Jr., Shaffer RN. Analysis of surgical and medical management of glaucoma in Sturge–Weber syndrome. Ophthalmology. 1990;97(7):904–9.PubMedCrossRef Iwach AG, Hoskins HD, Jr., Hetherington J, Jr., Shaffer RN. Analysis of surgical and medical management of glaucoma in Sturge–Weber syndrome. Ophthalmology. 1990;97(7):904–9.PubMedCrossRef
Metadaten
Titel
Histology after enucleation with Sturge–Weber syndrome
verfasst von
Dr. Fabian Mathias Bauer
Johann Colvin
Max Rasp
Eva Maria Krall
Eva Maria Arlt
Alexander Bachernegg
Alois Dexl
Martin Emesz
Publikationsdatum
01.11.2014
Verlag
Springer Vienna
Erschienen in
Spektrum der Augenheilkunde / Ausgabe 5/2014
Print ISSN: 0930-4282
Elektronische ISSN: 1613-7523
DOI
https://doi.org/10.1007/s00717-014-0229-2

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